Loading...
Dernières publications
-
Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
-
Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
-
Ingo Riederer, Daniella Arêas Mendes-Da-Cruz, Guilherme Cordenonsi da Fonseca, Mariela Natacha González, Otavio Brustolini, et al.. Zika virus disrupts gene expression in human myoblasts and myotubes: Relationship with susceptibility to infection. PLoS Neglected Tropical Diseases, 2022, 16 (2), pp.e0010166. ⟨10.1371/journal.pntd.0010166⟩. ⟨hal-03832616⟩
Chiffres clés
98
Publications avec texte intégral
Open Access
59 %
Mots clés
Adipose tissue
AChR antibodies
Satellite cell
Myopathies
Biomarker
DMD
Myogenesis
Myoblast
Nuclear envelope
Transcriptomics
Haploinsufficiency
AAV vectors
Agrégats de PABPN1
Atrophy
CD49d
Ageing
Metabolism
Dystrophin
Andermann syndrome
Cell therapy
Gene replacement
Muscle fibrosis
Autoimmune diseases
CNOT6L
Cross-bridge kinetics
Fibrosis
Satellite cells
PABPN1 agregates
Thérapie génique
Lamins
Arbovirus
Differentiation
Akt
Dysferlinopathy
GENE
Human
Muscle strength
Bioinformatics
Pharyngeal muscle
CS
Muscle
Dysferlin
Myoblasts
Myosin
Biopsies humaines
Inflammation
Exon-skipping
C2C12 cells
Bile salt hydrolases
DUX4
ARN
Antiserum
Aged
MUTATIONS
Triplet expansion disease
Actin
C2 domains
Intercellular communication
Alphavirus
RNA
APOPTOSIS
Anti-acetylcholine receptor antibodies
OPMD
Anti-fibrotic pharmacotherapies
Bioinformatique
Calcium
Skeletal muscle
Xenograft
Muscle dystrophy
FAPs
AUTOPHAGY
Functional genomics
Annexin A2
Aav-U7
ALS
DNA methylation
Botulinum neurotoxin
Gene therapy
Pax7
AAV
Myositis
2-D PAGE
Accelerometry
Geriatric assessment
Antisens oligonucleotides
FSHD
Aggregate
Duchenne muscular dystrophy
Alzheimer's disease
Autologous
BINDING SPECIFICITY
Sarcopenia
Regeneration
Myopathy
Oculopharyngeal muscular dystrophy
Myotube
PABPN1
Muscle stem cells
Dystrophie musculaire oculopharyngée
Neuromuscular junction NMJ