Comparison of echocardiographic parameters in Fabry cardiomyopathy and light-chain cardiac amyloidosis
Résumé
Fabry cardiomyopathy (FC) and light-chain amyloid cardiomyopathy (AL) present with concentric left ventricular (LV) hypertrophy/remodeling and diastolic rather than systolic dysfunction. Direct comparisons are difficult due to rarity and confounded by variability of LV thickness.